Ugeskr Læger 2015;177:V06140322
Renalt angiomyolipoma with spontaneous retroperitoneal bleeding
Angiomyolipoma (AML) is a benign tumour composed predominantly of blood vessels, smooth muscle tissue and adipose tissue. It is a rare disorder found in 0.1% of men and 0.22% of women. AML is most often manifested as a solitary tumor, but can also be found with multiple lesions in various organs. AML is predominantly asymptomatic, but may present with different symptoms depending on the size and position. Patients often have flank pain and microscopic or macroscopic haematuria. AML can also debut with spontaneous atraumatic bleeding in the retroperitoneum, Wunderlichs syndrome.