Dato3. jul 2017
Ugeskr Læger 2017;179:V02170155
Two cases of the rare Cronkhite-Canada syndrome
Cronkhite-Canada syndrome (CCS) is a rare non-heritable condition characterized by gastrointestinal polyposis, dysgeusia, malnutrition, total alopecia and onychodystrophia. Two Danish cases of CCS presented with signs of malnutrition, dyspepsia, vomiting, dysgeusia and hair loss. An upper endoscopy revealed marked oedema and polyposis in the stomach. Both patients developed colonic adenocarcinomas, which were radically operated. Treatment consisted of hyperalimentation, prednisolone and azathioprine. Both patients went into remission – the first patient totally.